Perfusion UPDATED ACTUAL Questions
and CORRECT Answers
How do you get CF? - CORRECT ANSWER - CF is a familial disease gotten from both parents
who were carriers.
Cystic Fibrosis: Etiology and Pathophysiology. - CORRECT ANSWER - Multisystem
involvement
Increased viscosity of mucous gland secretions
Elevation of sweat electrolytes
Increase in enzymatic constituents of saliva
Autonomic nervous system abnormalities
CF is an autosomal recessive disorder - CORRECT ANSWER - CF transmembrane regulator
(CFTR) protein localizes to epithelial surface of airways, pancreatic ducts, and sweat gland ducts
Alters ionic transport of sodium and chloride in the sweat
Obstruction of ducts of lungs, pancreas, and intestines is caused by thick, viscous secretions
Mucus fills (plugs up) glands in these organs
Causes glands to atrophy, ultimately resulting in organ failure
CF is an autosomal recessive disorder
Obstruction of ducts of lungs, pancreas, and intestines is caused by thick, viscous secretions - CORRECT
ANSWER - Mucus fills (plugs up) glands in these organs
Causes glands to atrophy, ultimately resulting in organ failure
, CF - CORRECT ANSWER - Autosomal recessive, multisystem disease
Test for CF - CORRECT ANSWER - sweat test
altered sodium and chloride ions in and out of epithelial cells of
*Lungs: excess secretions
*Pancreas and biliary tract
* Reproductive tract: males usually sterile (vast differens will not let sperm leave the testes), females can
still reproduce
CF diagnosis - CORRECT ANSWER - *First signs and symptoms usually occur in children
*Some patients are not diagnosed until adulthood
*Median life span is more than 41 years
__________________________________________________
Nursing ASSESSMENT:
- Tachycardia
- Foul, fatty stools
- Abdominal distention
- Abnormal ABGs
- X-ray
CF symptoms