USMLE EXAMzm
Exam Solution
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First Aid USMLE STEP 1 High Yield 2026 A+ GRADE ASS
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URED COMPLETE SOLUTIONS AND VERIFIED ANSWERS
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(1BE84)
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QUESTION 1 zm
Abdominal pain, ascites, and hepatomegaly
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ANSWER
Budd-Chiari syndrome (posthepatic venous thrombosis) -Absence of JVD
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QUESTION 2 zm
Abdominal pain, diarrhea, leukocytosis, recent antibiotic use
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ANSWER
Clostridium difficile infection
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QUESTION 3 zm
Achilles tendon xanthoma
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ANSWER
Familial hypercholesterolemia (decreased LDL receptor signaling)
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QUESTION 4 zm
Adrenal hemorrhage, hypotension, DIC
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ANSWER
Waterhouse-Friderichsen syndrome (menengococcemia) zm zm
,QUESTION 5 zm
Anaphylaxis following blood transfusion zm zm zm
ANSWER
IgA deficiency
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QUESTION 6 zm
Anterior "drawer sign" ⊕ zm zm zm
ANSWER
Anterior cruciate ligament injury
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QUESTION 7 zm
Arachnodactyly, lens dislocation, aortic dissection, hyperflexible joints
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ANSWER
Marfan syndrome (fibrillin defect)
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QUESTION 8 zm
Athlete with polycythemia
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ANSWER
2° to erythropoietin injection
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QUESTION 9 zm
Back pain, fever, night sweats
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ANSWER
Pott disease (vertebral TB)
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QUESTION 10 zm
Bilateral acoustic schwannomaszm zm
ANSWER
Neurofibromatosis type 2 zm zm
,QUESTION 11 zm
Bilateral hilar adenopathy, uveitis
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ANSWER
Sarcoidosis (noncaseating granulomas)
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QUESTION 12 zm
Black eschar on face of patient with diabetic ketoacidosis
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ANSWER
Mucor or Rhizopus fungal infection
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QUESTION 13 zm
Blue sclera, brittle bones
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ANSWER
Osteogenesis imperfecta (type I collagen defect)
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QUESTION 14 zm
Bluish line on gingiva
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ANSWER
Burton line (lead poisoning)
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QUESTION 15 zm
Bone pain, bone enlargement, arthritis
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ANSWER
Paget disease of bone (osteoblastic and osteoclastic activity)
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QUESTION 16 zm
Bounding pulses, diastolic heart murmur, head bobbing
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ANSWER
Aortic regurgitation
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, QUESTION 17 zm
"Butterfly" facial rash and Raynaud phenomenon in a young female
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ANSWER
Systemic lupus erythematosus
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QUESTION 18 zm
Café-au-
lait spots, Lisch nodules (iris hamartoma), cutaneous neurofibromas, pheochromocyto
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mas, optic gliomas
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ANSWER
Neurofibromatosis type I, pheochromocytoma, optic gliomas
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QUESTION 19 zm
Café-au-
lait spots (unilateral), polyostotic fibrous dysplasia, precocious puberty, multiple endo
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crine abnormalities
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ANSWER
McCune-Albright syndrome (mosaic G-protein signaling mutation)
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QUESTION 20 zm
Calf pseudohypertrophy
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ANSWER
Muscular dystrophy (most commonly Duchenne, due to X-
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linked recessive frameshift mutation of dystrophin gene)
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QUESTION 21 zm
Child with cervical lymphadenopathy, desquamating rash, coronary aneurysms, red co
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njunctivae and tongue zm zm
ANSWER
Kawasaki disease (treat with IVIG and aspirin)
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QUESTION 22 zm
Exam Solution
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First Aid USMLE STEP 1 High Yield 2026 A+ GRADE ASS
zm zm zm zm zm zm zm zm zm zm
URED COMPLETE SOLUTIONS AND VERIFIED ANSWERS
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(1BE84)
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QUESTION 1 zm
Abdominal pain, ascites, and hepatomegaly
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ANSWER
Budd-Chiari syndrome (posthepatic venous thrombosis) -Absence of JVD
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QUESTION 2 zm
Abdominal pain, diarrhea, leukocytosis, recent antibiotic use
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ANSWER
Clostridium difficile infection
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QUESTION 3 zm
Achilles tendon xanthoma
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ANSWER
Familial hypercholesterolemia (decreased LDL receptor signaling)
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QUESTION 4 zm
Adrenal hemorrhage, hypotension, DIC
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ANSWER
Waterhouse-Friderichsen syndrome (menengococcemia) zm zm
,QUESTION 5 zm
Anaphylaxis following blood transfusion zm zm zm
ANSWER
IgA deficiency
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QUESTION 6 zm
Anterior "drawer sign" ⊕ zm zm zm
ANSWER
Anterior cruciate ligament injury
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QUESTION 7 zm
Arachnodactyly, lens dislocation, aortic dissection, hyperflexible joints
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ANSWER
Marfan syndrome (fibrillin defect)
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QUESTION 8 zm
Athlete with polycythemia
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ANSWER
2° to erythropoietin injection
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QUESTION 9 zm
Back pain, fever, night sweats
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ANSWER
Pott disease (vertebral TB)
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QUESTION 10 zm
Bilateral acoustic schwannomaszm zm
ANSWER
Neurofibromatosis type 2 zm zm
,QUESTION 11 zm
Bilateral hilar adenopathy, uveitis
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ANSWER
Sarcoidosis (noncaseating granulomas)
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QUESTION 12 zm
Black eschar on face of patient with diabetic ketoacidosis
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ANSWER
Mucor or Rhizopus fungal infection
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QUESTION 13 zm
Blue sclera, brittle bones
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ANSWER
Osteogenesis imperfecta (type I collagen defect)
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QUESTION 14 zm
Bluish line on gingiva
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ANSWER
Burton line (lead poisoning)
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QUESTION 15 zm
Bone pain, bone enlargement, arthritis
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ANSWER
Paget disease of bone (osteoblastic and osteoclastic activity)
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QUESTION 16 zm
Bounding pulses, diastolic heart murmur, head bobbing
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ANSWER
Aortic regurgitation
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, QUESTION 17 zm
"Butterfly" facial rash and Raynaud phenomenon in a young female
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ANSWER
Systemic lupus erythematosus
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QUESTION 18 zm
Café-au-
lait spots, Lisch nodules (iris hamartoma), cutaneous neurofibromas, pheochromocyto
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mas, optic gliomas
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ANSWER
Neurofibromatosis type I, pheochromocytoma, optic gliomas
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QUESTION 19 zm
Café-au-
lait spots (unilateral), polyostotic fibrous dysplasia, precocious puberty, multiple endo
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crine abnormalities
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ANSWER
McCune-Albright syndrome (mosaic G-protein signaling mutation)
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QUESTION 20 zm
Calf pseudohypertrophy
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ANSWER
Muscular dystrophy (most commonly Duchenne, due to X-
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linked recessive frameshift mutation of dystrophin gene)
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QUESTION 21 zm
Child with cervical lymphadenopathy, desquamating rash, coronary aneurysms, red co
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njunctivae and tongue zm zm
ANSWER
Kawasaki disease (treat with IVIG and aspirin)
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QUESTION 22 zm