BIOCHEM 551 Quiz 6 Re-Updated- Louisiana University

 Question 1
1 out of 1 points
A patient diagnosed with Maple syrup urine disease will have
exacerbations of his symptoms when the patient consumes foods with
large amounts of these amino acids except__________?
Selected Threonine
Answer:

 Question 2
1 out of 1 points
Vitamin B12 deficiency results in hyperhomocysteinemia due to the
impaired activity of this enzyme of the methionine cycle;
Selected Methionine synthase
Answer:

 Question 3
1 out of 1 points
In a patient with biotin holocaboxylase synthetase deficiency, which of
these amino acids could be significantly elevated?
Selected Glycine
Answer:

 Question 4
1 out of 1 points
You are designing a nutritional plan for a patient that has been recently
diagnosed with biotin holocarboxylase deficiency. A rich nutritional
source of biotin to include in his meal plan is;
Selected All of the above
Answer:

 Question 5
1 out of 1 points
You have just got the lab results of a new patient of yours and it shows a
elevation of her serum homocysteine level, which of these is least likely
to be associated with increased serum homocysteine level?
Selected Liver disease
Answer:

 Question 6
1 out of 1 points
In which of these conditions will you expect a low serum level of free
biotin?
Selected Biotinidase deficiency
Answer:

 Question 7

, 1 out of 1 points
Hyperammonemia is a common finding in patients with biotinidase
deficiency due to a secondary inhibition of NAGS by;
Selected Propionic acid
Answer:

 Question 8
1 out of 1 points
The capacity of the gastric parietal cells to secrete intrinsic factor will be
increased by;
Selected All of the above
Answer:

 Question 9
1 out of 1 points
Biotin is not considered essential for this metabolic pathway;
Selected Glycogenolysis
Answer:

 Question 10
1 out of 1 points
The type of atrophic gastritis that is characterized by megaloblastic
anemia, histamine-fast achlorhydria and antibodies against the intrinsic
factor is;
Selected Pernicious anemia
Answer:

 Question 11
1 out of 1 points
Megaloblastic anemia is a common feature of these except;
Selected Vitamin C deficiency
Answer:

 Question 12
1 out of 1 points
You are evaluating a patient who presented with a pulmonary embolism
secondary to hyperhomocysteinemia; his serum Vitamin B12 and folate levels
are normal, methionine level is also low. Which is the most likely defective
enzyme?


Selected MTR
Answer: R


 Question 13
1 out of 1 points
Which of these can result in a masking of hematologic signs and