TestBankForPediatrics19thEditionByNelson2024.
, TestBankForPediatrics19thEditionByNelson2024.
WhichphaseofKawasakidiseaseisassociatedwithcoronaryaneurysms?
A. Acutefebrilephase
B. Subacutephase
C. Convalescentphase
D. Phasegofcomplications
E. Alloftheabove-ANSWER-1B.
Kawasakidiseasepresentswithcharacteristicallyhigh, gunremittingfeverand4outofthe5principalg
features:
Bilateralnonexudativebulbarconjunctivalinjectionwithlimbalsparing;
Erythemaoftheoralandpharyngealmucosawithstrawberrytongueanddry,crackedlips;Edema
gandgerythemagofgtheghandsgandgfeet;
Rashgofgvariousgformsg(scarlatiniform,gmaculopapular,gerythemagmultiforme);Nonsuppurat
ivecervicallymphadenopathy(usuallyunilateral,withnodesize>1.5cm).Acute gfebrilegphaseg-
gfevergandgthegacutegsignsgofgillnessgandgusuallyglastsg1-2wks
Subacutegfebrilegphaseg-
gdesquamation,gthrombocytosis,gcoronaryganeurysmsgandghighestriskgofgsuddengdeathgusu
allyglastsg2gwks
Convalescentgphaseg-gAllgclinicalgsignsghavegdisappearedguntilgESRgnormalizesgtypicallyg6-
8wksgaftergonsetgongillness
Source:Nelson'sTextbookofPediatrics19theditionp864
Agfourgyeargoldgpresentsgwithglow-
gradegfever,gintermittentgcrampygabdominalgpaingwithemesisandswollenkneesof3daysdur
ation.Apurpuricrashdistributedbelowthekneesofbothglowergextremitiesgisgnotedgongphysic
algexamination.gThisgpatientgmostglikelyghas:
A. Meningococcemia
B. Idiopathicthrombocytopenicpurpura
C. Henoch-Scholeinpurpura
D. SLEE.JuvenileRheumatoidarthritis-ANSWER-2C.
HSPgisgagcommongvasculitisgamonggchildrengandgpresentsgwithgthegclassicgfindingsgofabdo
minalgpaingwithgorgwithoutgrectalgbleeding,gvasculitisgrash,garthritisgandgnephritis.gTheplat
eletgcountgisgnormal.gGastrointestinalginvolvementgmaygprogressgtogintussusception.
Source:Nelson'sTextbookofPediatrics19theditionp868
Ag3gyeargoldgfemalegpresentsgwithg1gweekghistorygofgdailyg(quotidian)gfevergassociatedgwit
harthritisofbothanklesandherrightknee.Hermothernotesthatshehasdecreasedactivity
TestBankForPediatrics19thEditionByNelson2024.
, TestBankForPediatrics19thEditionByNelson2024.
andalsonotesrashesthatcomeandgoingdifferentpartsofherbodybutnotontheface.Onphysical g
examination,gsalmongcoloredgpatchesgweregnotedgongthegtrunkgandgextremities.Palpationgr
evealedgsplenomegaly.gWhatgisgthegdiagnosis?
A. HenochSchoenleinPurpura
B. SystemicLupusErythematosus
C. JuvenileRheumatoidarthritis
D. JuvenileDermatomyositis
E. Denguefever-ANSWER-3C.
Don'tgforgetgtogstudygrheumaticgdiseasesgofgchildhoodgevengifgit'sgnotgyourgfavoritegtopic.F
amiliarizegyourselfgwithgthegrelativelygcommongonesglikegJRA,gSLEandgdermatomyositis,HS
Pandscleroderma.Payattentiontothegcharacteristicsoftherashandotherfeatures.
(Don'tgfallgforgthegtrapgofgrashg+garthritisg=gSLE..gIt'sgnotgalwaysgSLE!)
JRA-Salmoncoloredpatch,evanescent,sparesthefaceSLE g-
gMalargrash,gphotosensitive
Dermatomyositis-heliotrope(periorbital)rash,gottronpapules(rashontheknuckles)HSP g-
gpurpuragingdependentgportions
ForJRA,knowthedifferencesbetweensubtypes(oligoarticularvspolyarticularvssystemiconset)
ThisgcasegingparticulargisgagcasegofgsystemicgonsetgJuvenilegRheumatoidgarthritisg(alsogcalledSt
ill'sgDisease)
Source:Nelson'sTextbookofPediatrics19theditionp830
Ag4gyrgoldgboygpresentsgwithghisgthirdgepisodegofgpainfulgcervicalglymphadenitis.gEachgwas
treatedgwithgincisiongandgdrainagegandggrewgS.gaureus.gHegalsogexperiencesgrecurrentgskin
infections.Ayearago,hewashospitalizedforosteomyelitis.Themostimportantlaboratorytest gis
:
A. PCRforADAdeficiency
B. Nitrobluetetrazoliumtest
C. MAC-Iassay
D. Neutrophilcount
E. Geneticgchromosomalganalysisg-gANSWERg-
g4gB.gThisgisgagcasegofgchronicggranulomatousdisease(CGD)whereinpatientsaresusceptiblet
ocatalasepositiveorganismslikeS.aureus.Thenitrobluetetrazoliumteststheneutrophilsability
togeneratesuperoxideanionandthuskillgingestedgbacteria.
Source:Nelson'sTextbookofPediatrics19theditionp746
TestBankForPediatrics19thEditionByNelson2024.
, TestBankForPediatrics19thEditionByNelson2024.
WhichamongthefollowingisnotaprominentfeatureofWiskott-Aldrichsyndrome?
A. X-linkedrecessiveinheritance
B. Atopicdermatitis
C. Thrombocytopenia
D. Recurrentinfectionswithencapsulatedbacteria
E. Leukopenia-ANSWER-5E.
Note:TheprominentimmunologicimpairmentinWiskottAldrichSyndromeisagainstpolysacchari
desgofgencapsulatedgorganisms
Source:Nelson'sTextbookofPediatrics19theditionp734
Ag12gyeargoldgseeksgconsultgforg1gdayghistorygofgsneezing,gcleargrhinorrheagandgnasalgitchi
ngnotgassociatedgwithgfevergorganygothergsystemicgsymptoms.gPEgrevealsgboggy,gpalegnasa
ledemagwithgagcleargdischarge.gThegmostglikelygdiagnosisgis?
A. Foreignbody
B. Vasomotorrhinitis
C. Allergicrhinitis
D. Neutrophilicrhinitis
E. Rhinitismedicamentosa-ANSWER-6C.
Allergicrhinitisisoftenseasonalandassociatedwithallergicconjunctivitis.Eosinophilspredominat
egingthegnasalgsecretions.gItgisgclassifiedgas:
Seasonal(cyclical)orperennial(allyear)
Intermittent(symptomsoccur<4daysperweekor<4consecutiveweeks)orpersistent(symptoms go
ccurg>4gdaysgpergweekgorg>4gconsecutivegweeks)
Mild-moderate(noimpairment)orsevere(withimpairmentofdailyliving/
sleep)Source:gNelson'sgTextbookgofgPediatricsg19thgeditiongp775
TheKasaiprocedureisindicatedforwhichofthefollowing?
A. Neonatalhepatitis
B. Biliaryatresia
C. Metabolicliverdisease
D. Fulminanthepaticfailure
E. Noneoftheaboveg-ANSWER-7B.
DespiteinitialsuccessoftheKasaioperation,patientswithbiliaryatresiaeventuallygetlivertranspla
ntation.
Source:Nelson'sTextbookofPediatrics19thedition1387
TestBankForPediatrics19thEditionByNelson2024.