STUDYSAGE
KSAP Volume 8 Module 1 study
set guide with detailed
questions and 100% accurate
answers.ALREADY GRADED A.
What is the normal daily osmolal excretion? - CORRECT ANSWERS✔️✔️600-
800/day
What is the Mayo imaging classification stratified into for ADPKD? - CORRECT
ANSWERS✔️✔️1A-1E (5 classes) with 1C-1E indicating rapid progression and
should be initiated on tolvaptan
ADTKD (previouslly called medullary cystic kidney disease) is caused by mutations
in some genes? - CORRECT ANSWERS✔️✔️UMOD -- benefit from tx of
hyperuricemia
REN -- may benefit from fludrocortisone
HNF1B
MUC1
SEC61A1
Caused my accumulation of misfolded proteins leading to inflammatory
infiltration and interstitial fibrosis
SUCCESS
,STUDYSAGE
What is the difference between Type A and Type B dissection? - CORRECT
ANSWERS✔️✔️Type A: involves ascending aorta. managem medically
Type B: no involvement of ascending aorta and managed medically with lowering
BP to 100-120 mmHg and controlling HR
What is the imaging modality of choice for aortic dissection - CORRECT
ANSWERS✔️✔️CTA
What are the clinical manifestations of hyperMg? - CORRECT
ANSWERS✔️✔️nausea/vomiting/headache
diminished deep tendon reflexes
hypotension
bradycardia
somnolence
muscle paralysis
CHB
cardiac arrest
What are the shape of crystals on urine microscopy in cystinuria? - CORRECT
ANSWERS✔️✔️hexagonal crystals
(stones are yellow/brown in appearance)
What happens in a patient with cysteinuria if you combine their urine with
cyanide-nipride? - CORRECT ANSWERS✔️✔️urine will turn purple!
SUCCESS
, STUDYSAGE
What are the kidney manifestations of tuberous sclerosis complex? - CORRECT
ANSWERS✔️✔️Ash leaf spots, facial angiofibromas
most common kidney finding is angiomyolipomas
What is the presentation of cystinosis - CORRECT ANSWERS✔️✔️cystine deposits
in the eyes --> photophobia, blepharospasm and visual loss
most common kidney manifestation is proteinuria and CKD
How does Fabry's disease present? - CORRECT ANSWERS✔️✔️angiokeratomas +
anhidrosis + corneal opacities
CKD is the kidney manifestation
How does Wilson's disease present? - CORRECT ANSWERS✔️✔️impaired biliary
copper excretion and low serum ceruloplasmin level
Copper accumulates in liver, brain and cornea. dysarthria
Kidney manifestation -- proximal and distal RTA
When does nephrotic syndrome after stem cell transplant occur? - CORRECT
ANSWERS✔️✔️>6 months typically
--> usually membranous, second most common is minimal change disease
SUCCESS
KSAP Volume 8 Module 1 study
set guide with detailed
questions and 100% accurate
answers.ALREADY GRADED A.
What is the normal daily osmolal excretion? - CORRECT ANSWERS✔️✔️600-
800/day
What is the Mayo imaging classification stratified into for ADPKD? - CORRECT
ANSWERS✔️✔️1A-1E (5 classes) with 1C-1E indicating rapid progression and
should be initiated on tolvaptan
ADTKD (previouslly called medullary cystic kidney disease) is caused by mutations
in some genes? - CORRECT ANSWERS✔️✔️UMOD -- benefit from tx of
hyperuricemia
REN -- may benefit from fludrocortisone
HNF1B
MUC1
SEC61A1
Caused my accumulation of misfolded proteins leading to inflammatory
infiltration and interstitial fibrosis
SUCCESS
,STUDYSAGE
What is the difference between Type A and Type B dissection? - CORRECT
ANSWERS✔️✔️Type A: involves ascending aorta. managem medically
Type B: no involvement of ascending aorta and managed medically with lowering
BP to 100-120 mmHg and controlling HR
What is the imaging modality of choice for aortic dissection - CORRECT
ANSWERS✔️✔️CTA
What are the clinical manifestations of hyperMg? - CORRECT
ANSWERS✔️✔️nausea/vomiting/headache
diminished deep tendon reflexes
hypotension
bradycardia
somnolence
muscle paralysis
CHB
cardiac arrest
What are the shape of crystals on urine microscopy in cystinuria? - CORRECT
ANSWERS✔️✔️hexagonal crystals
(stones are yellow/brown in appearance)
What happens in a patient with cysteinuria if you combine their urine with
cyanide-nipride? - CORRECT ANSWERS✔️✔️urine will turn purple!
SUCCESS
, STUDYSAGE
What are the kidney manifestations of tuberous sclerosis complex? - CORRECT
ANSWERS✔️✔️Ash leaf spots, facial angiofibromas
most common kidney finding is angiomyolipomas
What is the presentation of cystinosis - CORRECT ANSWERS✔️✔️cystine deposits
in the eyes --> photophobia, blepharospasm and visual loss
most common kidney manifestation is proteinuria and CKD
How does Fabry's disease present? - CORRECT ANSWERS✔️✔️angiokeratomas +
anhidrosis + corneal opacities
CKD is the kidney manifestation
How does Wilson's disease present? - CORRECT ANSWERS✔️✔️impaired biliary
copper excretion and low serum ceruloplasmin level
Copper accumulates in liver, brain and cornea. dysarthria
Kidney manifestation -- proximal and distal RTA
When does nephrotic syndrome after stem cell transplant occur? - CORRECT
ANSWERS✔️✔️>6 months typically
--> usually membranous, second most common is minimal change disease
SUCCESS
