Neurology Board Review - ABPN
maintenance Exam 2026 Questions and
Answers
seizure freedom from MTS resection - Correct answer-75%
schizencephaly - Correct answer-open goes to ventricles
closed does not go to ventricles
abnormal cortex up to the split
neural migration deficit
BCECTS or benign rolandic epilepsy - Correct answer-4 to 10 years
during sleep
semiology: perioral paresthesias and ipsilateral facial myoclonus, as well as
excessive salivation, speech arrest, and guttural noises.
EEG ihigh-amplitude, blunt, centrotemporal spikes with increased frequency
during sleep. Different from panayiotopolous which is also during sleep put +
autonomic features, emesis, and tonic eye deviation
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,progressive myoclonic epilepsy causes - Correct answer-can be associated with
cognitive decline and can be genetic +/- metabolic
-sialidosis (enzyme analysis)
-tay sachs
-MERFF (muscle bx)
-lafora body disase
-neuronal ceroid lipofuscinosis (skin bx for these 3)
-unverricht Kundborg, DRPLA (genetic testing)
SCN1A Gene - Correct answer-severe myoclonic epilepsy of infancy. (Dravets).
can have febrile status that is hemiconvulsive
Then develop unprovoked GTC.
Can develop ataxia
Development starts normal and then worsens after seizures
ATN1 Gene - Correct answer-DRPLA
(japenese and some AfAm in america)
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, AD
trinucleotide repeat
myoclonus/cogntive and emotional changes.
epilepsy with grand mal seizure on awakening - Correct answer-IS a real sz type of
idiopathic generalized seizure
EEG with genl discharges and photosensitivity
CACNA1A - Correct answer-multiple phenotypes: sporadic and familial migraine
-episodic ataxia
-SCA type 6
TSC1 - Correct answer-Tuberous sclerosis
ADNFLE - Correct answer-Autosomal Dominant Frontal Lobe epilepsy
- dx base on hx alone
When to do a skin bx for epilepsy - Correct answer-when progressive and with
cognitive decline
most common intramedullary spinal cord tumor in adults - Correct answer-
ependymoma
slow growing
©COPYRIGHT 2025, ALL RIGHTS RESERVED 3
maintenance Exam 2026 Questions and
Answers
seizure freedom from MTS resection - Correct answer-75%
schizencephaly - Correct answer-open goes to ventricles
closed does not go to ventricles
abnormal cortex up to the split
neural migration deficit
BCECTS or benign rolandic epilepsy - Correct answer-4 to 10 years
during sleep
semiology: perioral paresthesias and ipsilateral facial myoclonus, as well as
excessive salivation, speech arrest, and guttural noises.
EEG ihigh-amplitude, blunt, centrotemporal spikes with increased frequency
during sleep. Different from panayiotopolous which is also during sleep put +
autonomic features, emesis, and tonic eye deviation
©COPYRIGHT 2025, ALL RIGHTS RESERVED 1
,progressive myoclonic epilepsy causes - Correct answer-can be associated with
cognitive decline and can be genetic +/- metabolic
-sialidosis (enzyme analysis)
-tay sachs
-MERFF (muscle bx)
-lafora body disase
-neuronal ceroid lipofuscinosis (skin bx for these 3)
-unverricht Kundborg, DRPLA (genetic testing)
SCN1A Gene - Correct answer-severe myoclonic epilepsy of infancy. (Dravets).
can have febrile status that is hemiconvulsive
Then develop unprovoked GTC.
Can develop ataxia
Development starts normal and then worsens after seizures
ATN1 Gene - Correct answer-DRPLA
(japenese and some AfAm in america)
©COPYRIGHT 2025, ALL RIGHTS RESERVED 2
, AD
trinucleotide repeat
myoclonus/cogntive and emotional changes.
epilepsy with grand mal seizure on awakening - Correct answer-IS a real sz type of
idiopathic generalized seizure
EEG with genl discharges and photosensitivity
CACNA1A - Correct answer-multiple phenotypes: sporadic and familial migraine
-episodic ataxia
-SCA type 6
TSC1 - Correct answer-Tuberous sclerosis
ADNFLE - Correct answer-Autosomal Dominant Frontal Lobe epilepsy
- dx base on hx alone
When to do a skin bx for epilepsy - Correct answer-when progressive and with
cognitive decline
most common intramedullary spinal cord tumor in adults - Correct answer-
ependymoma
slow growing
©COPYRIGHT 2025, ALL RIGHTS RESERVED 3
